1.
Article
in English
| IMSEAR
| ID: sea-65122
ABSTRACT
We report a 5-year-old girl with congenital hepatic fibrosis who presented with clubbing and cyanosis. Partial pressure of oxygen was 40 mmHg with oxy-gen saturation of 70% on room air, which improved to 128 mmHg and 92% on inhalation of 100% oxygen. Macroaggregated albumin scan showed 58% shunting to the brain, suggestive of severe hepatopulmonary syndrome. Echocardiogram and pulmonary angiogram ruled out pulmonary hypertension. Four weeks after living-related liver transplantation, she had normal blood gases and reduction in shunting to 7% on macroaggregated albumin scan.
Subject(s)
Child, Preschool , Female , Follow-Up Studies , Hepatopulmonary Syndrome/complications , Humans , Liver Cirrhosis/congenital , Liver Transplantation , Living Donors , Technetium Tc 99m Aggregated Albumin/diagnosis , Treatment Outcome
2.
Indian Pediatr
;
1998 Aug; 35(8): 803
Article
in English
| IMSEAR
| ID: sea-7681
3.
Article
in English
| IMSEAR
| ID: sea-65677